The data of 10 congenital middle ear cholesteatoma (CMEC) patients with concurrent congenital ossicular anomalies (COAs), who were admitted to the Second Hospital of Jilin University between January 1, 2018, and July 31, 2025 were retrospectively reviewed. The cohort comprised 8 males and 2 females, with ages ranging from 4 to 36 years....
This 10-case series provides rare descriptive data on a co-occurring congenital condition; no practice change is warranted, but it may heighten clinical suspicion for ossicular malformation when diagnosing congenital middle ear cholesteatoma.
Congenital middle ear cholesteatoma co-occurring with ossicular malformation is rarely documented, and this case series contributes to the sparse literature that guides surgical decision-making in pediatric otology.
- 01Ten pediatric cases of congenital middle ear cholesteatoma with ossicular malformation reported from a single Chinese hospital.
- 02Both conditions occurring together is rare and diagnostically challenging.
- 03Case series describes clinical, radiological, and surgical findings.
- 04Small sample size (n=10) limits generalizability.
- 05Published in Zhonghua Yi Xue Za Zhi (Chinese Medical Journal), 2026.
Congenital middle ear cholesteatoma can co-occur with congenital ossicular malformation in pediatric patients.
studysupported- PMID
- 42297587
- DOI
- 10.3760/cma.j.cn112137-20260203-00387.
- Journal
- Zhonghua Yi Xue Za Zhi (Chinese Medical Journal)
- Publication type
- case_report
- Evidence level
- 4
- Sample size
- 10
- Population
- Pediatric patients with congenital middle ear cholesteatoma and concurrent congenital ossicular malformation at a Chinese hospital
- Intervention
- Clinical and surgical management of congenital middle ear cholesteatoma with ossicular malformation
Primary outcomes
Clinical, radiological, and surgical findings in congenital middle ear cholesteatoma with concurrent ossicular malformation