Audiologists and otolaryngologists managing patients with EVA and sudden hearing loss should note this review's synthesis of treatment outcomes, though the evidence base is likely limited by small, heterogeneous studies; current treatment decisions should be made in consultation with otology/ENT specialists pending stronger evidence.
Enlarged vestibular aqueduct is one of the most common identifiable causes of childhood sensorineural hearing loss, and a systematic synthesis of treatment outcomes directly informs clinical management of acute hearing episodes in this population.
- 01Systematic review synthesises treatment approaches (e.g., steroids, rest, activity restriction) and outcomes for sudden hearing loss in EVA.
- 02Enlarged vestibular aqueduct syndrome is among the most common radiologically identifiable causes of paediatric sensorineural hearing loss.
- 03Published in the Journal of Laryngology & Otology, a leading peer-reviewed ENT/audiology journal.
- 04Outcomes data for EVA-related sudden hearing loss are likely heterogeneous due to small individual study sizes.
- 05Findings relevant to paediatric audiologists, ENT surgeons, and genetic counsellors managing EVA families.
Specific treatment approaches can improve outcomes for sudden hearing loss occurring in enlarged vestibular aqueduct syndrome.
studypartially supportedEnlarged vestibular aqueduct syndrome is associated with episodic sudden hearing loss events.
studysupported- PMID
- 42227101
- DOI
- 10.1017/S0022215126105088.
- Journal
- Journal of Laryngology & Otology
- Publication type
- review
- Evidence level
- 2a
- Population
- Patients with enlarged vestibular aqueduct syndrome experiencing sudden sensorineural hearing loss
- Intervention
- Various treatments for sudden hearing loss in EVA (e.g., corticosteroids, activity restriction)
Primary outcomes
Hearing outcomes following treatment for sudden hearing loss in EVA; Comparative effectiveness of treatment approaches