Enlarged vestibular aqueduct (EVA) is one of the most common inner ear anomalies associated with sensorineural hearing loss (SNHL) in childhood. OBJECTIVE: This study aimed to investigate the prevalence of EH in patients with large vestibular aqueduct syndrome (LVAS).

Clinicians managing EVA patients should be aware of possible concurrent endolymphatic hydrops as a contributor to fluctuating hearing loss, though treatment protocol changes require confirmation from larger prospective studies.

Identifying a structural–pathophysiological link between EVA and endolymphatic hydrops could open new diagnostic and management pathways for pediatric and adult patients with this common inner-ear anomaly.

1. 01Investigates co-occurrence of enlarged vestibular aqueduct (EVA) and endolymphatic hydrops.
2. 02EVA is one of the most common identifiable causes of childhood sensorineural hearing loss.
3. 03Endolymphatic hydrops (excess inner-ear fluid pressure) may explain fluctuating hearing in EVA patients.
4. 04Published in Acta Otolaryngologica, a peer-reviewed otology journal.
5. 05Findings could influence diagnostic workup for EVA, potentially including hydrops imaging.

PMID

42115145

DOI

10.1080/00016489.2026.2668688.

Journal

Acta Otolaryngologica

Publication type

research_article

Evidence level

4

Population

Patients with enlarged vestibular aqueduct (EVA), likely including pediatric and adult cases

Intervention

Diagnostic investigation of endolymphatic hydrops in EVA patients