Incomplete Partition Type 3 (IP-III) is a rare congenital cochlear malformation and is associated with X-linked deafness radiologically characterized by the absence of the modiolus, absence of cribriform plate and an enlarged internal auditory canal (IAC) with preserved interscalar septa....
No actionable change for most audiologists; this single case report adds to the radiological characterization of a rare congenital inner ear malformation but does not alter established diagnostic or management pathways.
Detailed radiological case documentation of rare cochlear malformations like IP-III helps build the diagnostic reference literature needed to guide cochlear implant candidacy decisions in pediatric patients.
- 01IP-III is a rare congenital cochlear malformation associated with X-linked deafness.
- 02Diagnosis was made radiologically in a 4-year-old male.
- 03Case reports of IP-III are uncommon due to the rarity of the condition.
- 04Correct radiological identification of IP-III is critical before cochlear implantation.
- 05Published in Radiology Case Reports.
Cochlear incomplete partition type 3 (IP-III) can be identified radiologically in pediatric patients.
studysupportedIP-III is associated with X-linked deafness.
studysupported- PMID
- 42221973
- DOI
- 10.1016/j.radcr.2026.04.050.
- Journal
- Radiology Case Reports
- Publication type
- case_report
- Evidence level
- 4
- Sample size
- 1
- Population
- 4-year-old male with congenital cochlear malformation (IP-III)
- Intervention
- Radiological imaging for diagnosis of cochlear incomplete partition type 3
Primary outcomes
Radiological characterization of cochlear IP-III malformation